"Erdheim-Chester Disease" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
| Descriptor ID |
D031249
|
| MeSH Number(s) |
C15.604.250.410.224
|
| Concept/Terms |
|
Below are MeSH descriptors whose meaning is more general than "Erdheim-Chester Disease".
Below are MeSH descriptors whose meaning is more specific than "Erdheim-Chester Disease".
This graph shows the total number of publications written about "Erdheim-Chester Disease" by people in this website by year, and whether "Erdheim-Chester Disease" was a major or minor topic of these publications.
To see the data from this visualization as text,
click here.
| Year | Major Topic | Minor Topic | Total |
|---|
| 2012 | 2 | 0 | 2 |
| 2017 | 5 | 2 | 7 |
| 2018 | 8 | 0 | 8 |
| 2019 | 4 | 0 | 4 |
| 2020 | 1 | 0 | 1 |
To return to the timeline, click here.
Below are the most recent publications written about "Erdheim-Chester Disease" by people in Profiles.
-
Highlights of the Management of Adult Histiocytic Disorders: Langerhans Cell Histiocytosis, Erdheim-Chester Disease, Rosai-Dorfman Disease, and Hemophagocytic Lymphohistiocytosis. Clin Lymphoma Myeloma Leuk. 2021 01; 21(1):e66-e75.
-
Erdheim-Chester disease associated with chronic myelomonocytic leukemia harboring the same clonal mutation. Haematologica. 2019 11; 104(11):e530-e533.
-
Systemic Histiocytosis (Langerhans Cell Histiocytosis, Erdheim-Chester Disease, Destombes-Rosai-Dorfman Disease): from Oncogenic Mutations to Inflammatory Disorders. Curr Oncol Rep. 2019 05 21; 21(7):62.
-
Sarcoidosis occurring during BRAF/MEK inhibitors is associated with paradoxical ERK activation in Erdheim-Chester patients. J Eur Acad Dermatol Venereol. 2019 10; 33(10):e348-e350.
-
Autoimmunity associated with Erdheim-Chester disease improves with BRAF/MEK inhibitors. Haematologica. 2019 11; 104(11):e502-e505.
-
Cardiovascular Manifestations of Erdheim-Chester's Disease: A Case Series. Arq Bras Cardiol. 2018 12; 111(6):852-855.
-
Hypoalphalipoproteinemia and BRAFV600E Mutation Are Major Predictors of Aortic Infiltration in the Erdheim-Chester Disease. Arterioscler Thromb Vasc Biol. 2018 08; 38(8):1913-1925.
-
Prognostic factors of Erdheim-Chester disease: a nationwide survey in Japan. Haematologica. 2018 11; 103(11):1815-1824.
-
Treating Heart Inflammation With Interleukin-1 Blockade in a Case of Erdheim-Chester Disease. Front Immunol. 2018; 9:1233.
-
Erdheim-Chester disease: description of two illustrative cases involving the lung. Histopathology. 2018 Jul; 73(1):167-172.