Creutzfeldt-Jakob Syndrome
"Creutzfeldt-Jakob Syndrome" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
| Descriptor ID |
D007562
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| MeSH Number(s) |
C10.228.140.380.165 C10.228.228.800.230 F03.615.400.300
|
| Concept/Terms |
Creutzfeldt-Jakob Syndrome- Creutzfeldt-Jakob Syndrome
- Creutzfeldt Jakob Syndrome
- Syndrome, Creutzfeldt-Jakob
- Creutzfeldt-Jakob Disease
- Creutzfeldt Jakob Disease
- Disease, Creutzfeldt-Jakob
- Jakob-Creutzfeldt Disease
- Disease, Jakob-Creutzfeldt
- Jakob Creutzfeldt Disease
- CJD (Creutzfeldt-Jakob Disease)
- CJD (Creutzfeldt Jakob Disease)
- Spongiform Encephalopathy, Subacute
- Encephalopathies, Subacute Spongiform
- Encephalopathy, Subacute Spongiform
- Spongiform Encephalopathies, Subacute
- Subacute Spongiform Encephalopathies
- Subacute Spongiform Encephalopathy
- Creutzfeldt Jacob Disease
- Disease, Creutzfeldt Jacob
- Jacob Disease, Creutzfeldt
- Jakob-Creutzfeldt Syndrome
- Jakob Creutzfeldt Syndrome
- Syndrome, Jakob-Creutzfeldt
Creutzfeldt-Jakob Disease, Familial- Creutzfeldt-Jakob Disease, Familial
- Creutzfeldt Jakob Disease, Familial
- Creutzfeldt-Jakob Diseases, Familial
- Disease, Familial Creutzfeldt-Jakob
- Familial Creutzfeldt-Jakob Diseases
- Familial Creutzfeldt-Jakob Disease
- Familial Creutzfeldt Jakob Disease
New Variant Creutzfeldt-Jakob Disease- New Variant Creutzfeldt-Jakob Disease
- New Variant Creutzfeldt Jakob Disease
- Creutzfeldt-Jakob Disease, Variant
- Creutzfeldt Jakob Disease, Variant
- Creutzfeldt-Jakob Disease, New Variant
- Creutzfeldt Jakob Disease, New Variant
- Variant Creutzfeldt-Jakob Disease
- Variant Creutzfeldt Jakob Disease
- V-CJD (Variant-Creutzfeldt-Jakob Disease)
- V CJD (Variant Creutzfeldt Jakob Disease)
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Below are MeSH descriptors whose meaning is more general than "Creutzfeldt-Jakob Syndrome".
Below are MeSH descriptors whose meaning is more specific than "Creutzfeldt-Jakob Syndrome".
This graph shows the total number of publications written about "Creutzfeldt-Jakob Syndrome" by people in this website by year, and whether "Creutzfeldt-Jakob Syndrome" was a major or minor topic of these publications.
To see the data from this visualization as text,
click here.
| Year | Major Topic | Minor Topic | Total |
|---|
| 1995 | 1 | 0 | 1 |
| 1996 | 1 | 0 | 1 |
| 1999 | 1 | 0 | 1 |
| 2003 | 0 | 1 | 1 |
| 2004 | 1 | 0 | 1 |
| 2016 | 1 | 0 | 1 |
| 2017 | 2 | 0 | 2 |
| 2018 | 4 | 1 | 5 |
| 2019 | 1 | 0 | 1 |
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Below are the most recent publications written about "Creutzfeldt-Jakob Syndrome" by people in Profiles.
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Creutzfeldt-Jakob disease surveillance in Australia: update to 31 December 2020. Commun Dis Intell (2018). 2021 Jul 22; 45.
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Application of telehealth for comprehensive Creutzfeldt-Jakob disease surveillance in the United Kingdom. J Neurol Sci. 2021 01 15; 420:117221.
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Creutzfeldt-Jakob disease in a man with COVID-19: SARS-CoV-2-accelerated neurodegeneration? Brain Behav Immun. 2020 10; 89:601-603.
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Atypical clinical presentation of variant Creutzfeldt-Jakob disease. Eur J Anaesthesiol. 2019 09; 36(9):714-715.
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Drug-induced Creutzfeldt-Jakob disease-like syndrome: early CSF analysis as useful tool for differential diagnosis. BMJ Case Rep. 2018 Dec 04; 11(1).
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Distinct microglia profile in Creutzfeldt-Jakob disease and Alzheimer's disease is independent of disease kinetics. Neuropathology. 2018 Dec; 38(6):591-600.
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Clinical Reasoning: Rapidly progressive dementia in a patient with HIV after an exotic journey. Neurology. 2018 10 02; 91(14):e1360-e1364.
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Sporadic Fatal Insomnia in Europe: Phenotypic Features and Diagnostic Challenges. Ann Neurol. 2018 09; 84(3):347-360.
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Validation and utilization of amended diagnostic criteria in Creutzfeldt-Jakob disease surveillance. Neurology. 2018 07 24; 91(4):e331-e338.
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Inhibition of IL-1ß Signaling Normalizes NMDA-Dependent Neurotransmission and Reduces Seizure Susceptibility in a Mouse Model of Creutzfeldt-Jakob Disease. J Neurosci. 2017 10 25; 37(43):10278-10289.